Adult Vitelliform Macular Dystrophy

Adult Vitelliform Macular Dystrophy is closely related to Best’s disease. One out of four people with the adult-onset form of this disease has a genetic mutation that causes a fatty, yellow, fluid-filled protein to form beneath the pigment epithelial layer of the retina. In three out of four cases, there is no genetic mutation, and the exact cause for the protein formation is unknown.

In any case, the fluid-filled drusen will eventually rupture, and straight-ahead vision will slowly begin to worsen. Adult vitelliform macular dystrophy cannot be cured, but it is possible to adapt quite well to limited vision. Side (peripheral) vision and night vision will not be affected. This is because the disease affects the macula, and the macula is packed with cones. Rods, the photoreceptors of the retina that enable vision in conditions of low light, are not affected.

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